{"id":13418,"date":"2023-01-11T16:19:36","date_gmt":"2023-01-11T07:19:36","guid":{"rendered":"http:\/\/cell.brc.riken.jp\/ja\/?page_id=13418"},"modified":"2026-01-28T09:52:03","modified_gmt":"2026-01-28T00:52:03","slug":"ga-als","status":"publish","type":"page","link":"http:\/\/cell.brc.riken.jp\/ja\/hps\/hps_diseaselist_index\/ga-als","title":{"rendered":"\u7b4b\u840e\u7e2e\u6027\u5074\u7d22\u786c\u5316\u75c7\uff08ALS\uff09\u60a3\u8005\u7531\u6765iPS\u7d30\u80de\u306e\u907a\u4f1d\u5b50\u89e3\u6790\u60c5\u5831"},"content":{"rendered":"<p>\u5f53\u5ba4\u306b\u5bc4\u8a17\u3055\u308c\u3066\u3044\u308b\u7b4b\u840e\u7e2e\u6027\u5074\u7d22\u786c\u5316\u75c7 \/ Amyotrophic Lateral Sclerosis (ALS) \u60a3\u8005\u7531\u6765iPS\u7d30\u80de\u306b\u3064\u3044\u3066\u3001\u539f\u56e0\u907a\u4f1d\u5b50\u3068\u8003\u3048\u3089\u308c\u3066\u3044\u308bSOD1\u907a\u4f1d\u5b50\u304a\u3088\u3073TARDBP \/ ALS10 \/ TDP-43\u907a\u4f1d\u5b50\u306e\u5909\u7570\u306b\u3064\u3044\u3066\u89e3\u6790\u3092\u884c\u3063\u305f\u3002<\/p>\r\n\r\n<p>\u5bfe\u8c61\u7d30\u80de\u682a\uff1a61\u7d30\u80de\uff0861\u60a3\u8005\uff09<\/p>\r\n\r\n<p>\u89e3\u6790\u65b9\u6cd5\uff1aSOD1\u3068TARDB\u306e\u5168\u30a8\u30af\u30bd\u30f3\u3092\u7db2\u7f85\u3059\u308bIon AmpliSeq\u2122 On-Demand panel\u3092\u5229\u7528\u3057\u305fNGS (Ion S5) \u306b\u3088\u308b\u30bf\u30fc\u30b2\u30c3\u30c8\u30b7\u30fc\u30b1\u30f3\u30b9<\/p>\r\n\r\n\u7d50\u679c\uff1a\r\n<ul>\r\n <li>SOD1\u907a\u4f1d\u5b50\u306e\u5909\u7570\u3092\u691c\u51fa\uff1a8\u7d30\u80de\uff088\u60a3\u8005\uff09<\/li>\r\n <li>TARDBP \/ ALS10 \/ TDP-43\u907a\u4f1d\u5b50\u306e\u5909\u7570\u3092\u691c\u51fa\uff1a2\u7d30\u80de\uff082\u60a3\u8005\uff09<\/li>\r\n <li>SOD1\u907a\u4f1d\u5b50\u304a\u3088\u3073TARDBP \/ ALS10 \/ TDP-43\u907a\u4f1d\u5b50\u306e\u5909\u7570\u3092\u672a\u691c\u51fa\uff1a51\u7d30\u80de\uff0851\u60a3\u8005\uff09<\/li>\r\n<\/ul>\r\n\r\nMutations in SOD1\r\n\n<table id=\"tablepress-219\" class=\"tablepress tablepress-id-219\">\n<thead>\n<tr class=\"row-1\">\n\t<th class=\"column-1\">Cell No.<\/strong><\/th><th class=\"column-2\">Age<\/strong><\/th><th class=\"column-3\">Sex<\/strong><\/th><th class=\"column-4\">Exon<\/strong><\/th><th class=\"column-5\">Locus<\/strong><\/th><th class=\"column-6\">Coding<\/strong><\/th><th class=\"column-7\">Amino Acid Change<\/strong><\/th><th class=\"column-8\">homo or hetero<\/strong><\/th><th class=\"column-9\">other clones derived from the same patient<\/strong><\/th>\n<\/tr>\n<\/thead>\n<tbody class=\"row-striping row-hover\">\n<tr class=\"row-2\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0250&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0250<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">F<\/td><td class=\"column-4\">2<\/td><td class=\"column-5\">chr21:33036170<\/td><td class=\"column-6\">c.140A>G<\/td><td class=\"column-7\">p.His47Arg<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><\/td>\n<\/tr>\n<tr class=\"row-3\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0476&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0476<\/a><\/td><td class=\"column-2\">50s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">2<\/td><td class=\"column-5\">chr21:33036170<\/td><td class=\"column-6\">c.140A>G<\/td><td class=\"column-7\">p.His47Arg<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0477&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0477<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0478&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0478<\/a><\/td>\n<\/tr>\n<tr class=\"row-4\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0485&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0485<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">F<\/td><td class=\"column-4\">2<\/td><td class=\"column-5\">chr21:33036170<\/td><td class=\"column-6\">c.140A>G<\/td><td class=\"column-7\">p.His47Arg<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0486&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0486<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0487&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0487<\/a><\/td>\n<\/tr>\n<tr class=\"row-5\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0564&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0564<\/a><\/td><td class=\"column-2\">30s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">2<\/td><td class=\"column-5\">chr21:33036170<\/td><td class=\"column-6\">c.140A>G<\/td><td class=\"column-7\">p.His47Arg<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0565&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0565<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0566&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0566<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0567&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0567<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0568&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0568<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0569&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0569<\/a><\/td>\n<\/tr>\n<tr class=\"row-6\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0059&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0059<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">4<\/td><td class=\"column-5\">chr21:33039650<\/td><td class=\"column-6\">c.319C>G<\/td><td class=\"column-7\">p.Leu107Val<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><\/td>\n<\/tr>\n<tr class=\"row-7\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0558&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0558<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">4<\/td><td class=\"column-5\">chr21:33039650<\/td><td class=\"column-6\">c.319C>G<\/td><td class=\"column-7\">p.Leu107Val<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0559&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0559<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0560&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0560<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0561&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0561<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0562&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0562<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0563&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0563<\/a><\/td>\n<\/tr>\n<tr class=\"row-8\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0251&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0251<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">5<\/td><td class=\"column-5\">chr21:33040855<\/td><td class=\"column-6\">c.430_434dup<\/td><td class=\"column-7\">p.Leu145PhefsTer7<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1719&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS1719<\/a><\/td>\n<\/tr>\n<tr class=\"row-9\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0252&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0252<\/a><\/td><td class=\"column-2\">40s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">5<\/td><td class=\"column-5\">chr21:33040855<\/td><td class=\"column-6\">c.430_434dup<\/td><td class=\"column-7\">p.Leu145PhefsTer7<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1720&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS1720<\/a><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\r\n\r\nMutations in TARDBP \/ ALS10 \/ TDP-43\r\n\n<table id=\"tablepress-220\" class=\"tablepress tablepress-id-220\">\n<thead>\n<tr class=\"row-1\">\n\t<th class=\"column-1\">Cell No.<\/th><th class=\"column-2\">Age<\/th><th class=\"column-3\">Sex<\/th><th class=\"column-4\">Exon<\/th><th class=\"column-5\">Locus<\/th><th class=\"column-6\">Coding<\/th><th class=\"column-7\">Amino Acid Change<\/th><th class=\"column-8\">homo or hetero<\/th><th class=\"column-9\">other clones derived from the same patient<\/th>\n<\/tr>\n<\/thead>\n<tbody class=\"row-striping row-hover\">\n<tr class=\"row-2\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0290&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0290<\/a><\/td><td class=\"column-2\">50s<\/td><td class=\"column-3\">M<\/td><td class=\"column-4\">6<\/td><td class=\"column-5\">chr1:11082494<\/td><td class=\"column-6\">c.1028A>G<\/td><td class=\"column-7\">p.Gln343Arg<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0291&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0291<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0327&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0327<\/a><\/td>\n<\/tr>\n<tr class=\"row-3\">\n\t<td class=\"column-1\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0292&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0292<\/a><\/td><td class=\"column-2\">60s<\/td><td class=\"column-3\">F<\/td><td class=\"column-4\">6<\/td><td class=\"column-5\">chr1:11082475<\/td><td class=\"column-6\">c.1009A>G<\/td><td class=\"column-7\">p.Met337Val<\/td><td class=\"column-8\">hetero<\/td><td class=\"column-9\"><a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0293&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0293<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0294&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS0294<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1717&amp;lang=Ja\" rel=\"noopener\" target=\"_blank\">HPS1717<\/a><\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\r\n\r\nSOD1\u907a\u4f1d\u5b50\u304a\u3088\u3073TARDBP \/ ALS10 \/ TDP-43\u907a\u4f1d\u5b50\u306e\u5909\u7570\u3092\u672a\u691c\u51fa\u306e\u7d30\u80de<br>\r\n<a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0129&#038;lang=Ja\">HPS0129<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0134&#038;lang=Ja\">HPS0134<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0140&#038;lang=Ja\">HPS0140<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0146&#038;lang=Ja\">HPS0146<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0247&#038;lang=Ja\">HPS0247<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0248&#038;lang=Ja\">HPS0248<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0253&#038;lang=Ja\">HPS0253<\/a>, <a  href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0419&#038;lang=Ja\">HPS0419<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0473&#038;lang=Ja\">HPS0473<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0576&#038;lang=Ja\">HPS0576<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0612&#038;lang=Ja\">HPS0612<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0618&#038;lang=Ja\">HPS0618<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0624&#038;lang=Ja\">HPS0624<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0630&#038;lang=Ja\">HPS0630<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0636&#038;lang=Ja\">HPS0636<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0642&#038;lang=Ja\">HPS0642<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0648&#038;lang=Ja\">HPS0648<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0724&#038;lang=Ja\">HPS0724<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0730&#038;lang=Ja\">HPS0730<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0736&#038;lang=Ja\">HPS0736<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0742&#038;lang=Ja\">HPS0742<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0748&#038;lang=Ja\">HPS0748<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0754&#038;lang=Ja\">HPS0754<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0760&#038;lang=Ja\">HPS0760<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0766&#038;lang=Ja\">HPS0766<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0782&#038;lang=Ja\">HPS0782<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0788&#038;lang=Ja\">HPS0788<\/a>. <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0794&#038;lang=Ja\">HPS0794<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0824&#038;lang=Ja\">HPS0824<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0860&#038;lang=Ja\">HPS0860<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0878&#038;lang=Ja\">HPS0878<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0890&#038;lang=Ja\">HPS0890<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0896&#038;lang=Ja\">HPS0896<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0902&#038;lang=Ja\">HPS0902<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0908&#038;lang=Ja\">HPS0908<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0914&#038;lang=Ja\">HPS0914<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0920&#038;lang=Ja\">HPS0920<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS0926&#038;lang=Ja\">HPS0926<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1055&#038;lang=Ja\">HPS1055<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1056&#038;lang=Ja\">HPS1056<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1721&#038;lang=Ja\">HPS1721<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1818&#038;lang=Ja\">HPS1818<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1819&#038;lang=Ja\">HPS1819<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1821&#038;lang=Ja\">HPS1821<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1822&#038;lang=Ja\">HPS1822<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1824&#038;lang=Ja\">HPS1824<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1826&#038;lang=Ja\">HPS1826<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1828&#038;lang=Ja\">HPS1828<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1830&#038;lang=Ja\">HPS1830<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1831&#038;lang=Ja\">HPS1831<\/a>, <a href=\"https:\/\/cellbank.brc.riken.jp\/cell_bank\/CellInfo\/?cellNo=HPS1835&#038;lang=Ja\">HPS1835<\/a> <\/p>\r\n\r\n\r\n<p><\/p>\r\n","protected":false},"excerpt":{"rendered":"<p>\u5f53\u5ba4\u306b\u5bc4\u8a17\u3055\u308c\u3066\u3044\u308b\u7b4b\u840e\u7e2e\u6027\u5074\u7d22\u786c\u5316\u75c7 \/ Amyotrophic Lateral Sclerosis (ALS) \u60a3\u8005\u7531\u6765iPS\u7d30\u80de\u306b\u3064\u3044\u3066\u3001\u539f\u56e0\u907a\u4f1d\u5b50\u3068\u8003\u3048\u3089\u308c\u3066\u3044\u308bSOD1\u907a\u4f1d\u5b50\u304a\u3088\u3073TARDBP \/ ALS10 \/ TDP-43\u907a\u4f1d\u5b50\u306e\u5909\u7570\u306b\u3064\u3044\u3066\u89e3\u6790\u3092\u884c\u3063\u305f\u3002 \u5bfe\u8c61\u7d30\u80de\u682a\uff1a61\u7d30\u80de\uff0861\u60a3\u8005\uff09 \u89e3\u6790\u65b9\u6cd5\uff1aSOD1\u3068TARDB\u306e\u5168\u30a8\u30af\u30bd\u30f3\u3092\u7db2\u7f85\u3059\u308bIon AmpliSeq\u2122 On-Dema [&hellip;]<\/p>\n","protected":false},"author":103,"featured_media":0,"parent":10660,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_seopress_titles_title":"","_seopress_titles_desc":"","_seopress_robots_index":"","_seopress_robots_follow":"","_seopress_robots_imageindex":"","_seopress_robots_snippet":"","_seopress_robots_primary_cat":"","_seopress_robots_breadcrumbs":"","_seopress_robots_freeze_modified_date":"","_seopress_robots_custom_modified_date":"","_seopress_robots_canonical":"","_seopress_social_fb_title":"","_seopress_social_fb_desc":"","_seopress_social_fb_img":"","_seopress_social_fb_img_attachment_id":0,"_seopress_social_fb_img_width":0,"_seopress_social_fb_img_height":0,"_seopress_social_twitter_title":"","_seopress_social_twitter_desc":"","_seopress_social_twitter_img":"","_seopress_social_twitter_img_attachment_id":0,"_seopress_social_twitter_img_width":0,"_seopress_social_twitter_img_height":0,"_seopress_redirections_value":"","_seopress_redirections_enabled":"","_seopress_redirections_enabled_regex":"","_seopress_redirections_logged_status":"both","_seopress_redirections_param":"","_seopress_redirections_type":301,"_seopress_analysis_target_kw":"","_mc_calendar":[],"footnotes":"","_wp_rev_ctl_limit":""},"class_list":["post-13418","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/pages\/13418","targetHints":{"allow":["GET"]}}],"collection":[{"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/users\/103"}],"replies":[{"embeddable":true,"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/comments?post=13418"}],"version-history":[{"count":9,"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/pages\/13418\/revisions"}],"predecessor-version":[{"id":15525,"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/pages\/13418\/revisions\/15525"}],"up":[{"embeddable":true,"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/pages\/10660"}],"wp:attachment":[{"href":"http:\/\/cell.brc.riken.jp\/ja\/wp-json\/wp\/v2\/media?parent=13418"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}